Adams Oliver syndrome with evidence of periventricular calcifications on brain CT-scan
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Abstract
Adams Oliver syndrome is a very a rare genetic disorder with some of its manifestations commonly attributed to congenital infection or administration of medications during pregnancy. Adams Oliver syndrome should be considered patients with terminal transverse limb deficiencies and scalp defects. Limb defect is typically bilateral and asymmetrical. The syndrome can also be associated cardiovascular system such as obstructive lesions of the left heart which includes aortic stenosis. Lin et al emphasize that about 20% of patients with Adams Oliver syndrome have a cardiovascular malformations, frequently obstructive lesions of the left heart.
Intracranial calcification is a well recognized rare manifestation of Adams Oliver syndrome which has not been reported before in Iraq. The  aim of this paper is to describe the first case of this syndrome in Iraq which was associated with periventricular calcifications.
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References
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